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The first total vertebral involvement of benign fibrous histiocytoma: A case report and literature review.

ABSTRACT:

Background

Benign fibrous histiocytoma (BFH) is a rare bone tumor, extremely seldom in the spine.

Methods

We present a 52-year-old patient diagnosed with a BFH in the thoracic spine treated with total en bloc spondylectomy. A review of the published literature was also conducted.

Results

Non-ossifying fibroma (NOF) and BFH are named as one tumor called NOF/BFH. A total of 20 spinal BFHs have been previously reported, mainly involving the posterior elements. We present a BFH with total vertebral involvement. Curettage and excision are the main treatment options with limited recurrence.

Conclusions

This is the first total vertebral BFH up to now. Spinal BFH occupies rather low aggressiveness. With rather limited recurrence and malignant degeneration, surgical interventions seem enough for its management.

SUBMITTER: Yang J

PROVIDER: S-EPMC6940612 | biostudies-literature | 2020 Feb

REPOSITORIES: biostudies-literature

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Publications

The first total vertebral involvement of benign fibrous histiocytoma: A case report and literature review.

Yang Jian J Zhong Nanzhe N Hu Jinbo J Yang Xinghai X Xiao Jianru J

Journal of bone oncology 20191220

<h4>Background</h4>Benign fibrous histiocytoma (BFH) is a rare bone tumor, extremely seldom in the spine.<h4>Methods</h4>We present a 52-year-old patient diagnosed with a BFH in the thoracic spine treated with total en bloc spondylectomy. A review of the published literature was also conducted.<h4>Results</h4>Non-ossifying fibroma (NOF) and BFH are named as one tumor called NOF/BFH. A total of 20 spinal BFHs have been previously reported, mainly involving the posterior elements. We present a BFH ...[more]

PMID: 31908914

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