Oxidative Stress and Endoplasmic Reticulum Stress in Rare Respiratory Diseases.
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ABSTRACT:
SUBMITTER: Magallon M
PROVIDER: S-EPMC8003245 | biostudies-literature | 2021 Mar
REPOSITORIES: biostudies-literature
Publications
Oxidative Stress and Endoplasmic Reticulum Stress in Rare Respiratory Diseases.
Magallón María M Pastor Sara S Carrión Ana Esther AE Bañuls Lucía L Pellicer Daniel D Castillo Silvia S Bondía Sergio S Navarro-García María Mercedes MM González Cruz C Dasí Francisco F
Journal of clinical medicine 20210318 6
Several studies have shown that some rare respiratory diseases, such as alpha-1 antitrypsin deficiency (AATD), idiopathic pulmonary fibrosis (IPF), cystic fibrosis (CF), and primary ciliary dyskinesia (PCD) present oxidative stress (OS) and endoplasmic reticulum (ER) stress. Their involvement in these pathologies and the use of antioxidants as therapeutic agents to minimize the effects of OS are discussed in this review. ...[more]
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