Congenital portosystemic shunt with multiple splenic artery aneurysms: Reversing pulmonary hypertension and preventing aneurysm rupture.
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ABSTRACT:
SUBMITTER: Subramanian AP
PROVIDER: S-EPMC9802628 | biostudies-literature | 2022 May-Jun
REPOSITORIES: biostudies-literature
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Congenital portosystemic shunt with multiple splenic artery aneurysms: Reversing pulmonary hypertension and preventing aneurysm rupture.
Subramanian Anand P AP Bharath Adaligere Paraswanath AP Barthur Ashita A Jayranganath Mahimarangaiah M
Annals of pediatric cardiology 20220501 3
We report an unusual occurrence of multiple splenic artery aneurysms and splenomegaly in a young woman with severe pulmonary hypertension, secondary to a congenital portosystemic shunt (CPS). The splenic artery was occluded using an Amplatzer Duct Occluder-II device, and closure of the large intrahepatic CPS was achieved using a muscular ventricular septal defect occluder. There was resolution of splenomegaly with normal pulmonary artery pressures, a few months after the procedure. ...[more]
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