Ontology highlight
ABSTRACT:
SUBMITTER: Calatroni M
PROVIDER: S-EPMC5420084 | biostudies-literature | 2017 May
REPOSITORIES: biostudies-literature
Italian journal of pediatrics 20170505 1
Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitides are rare systemic diseases that usually occur in adulthood. They comprise granulomatosis with polyangiitis (GPA, Wegener's), microscopic polyangiitis (MPA) and eosinophilic granulomatosis with polyangiitis (EGPA, Churg-Strauss syndrome). Their clinical presentation is often heterogeneous, with frequent involvement of the respiratory tract, the kidney, the skin and the joints. ANCA-associated vasculitis is rare in childhood but N ...[more]